You Searched For: Ethyl+2-hydroxyisobutyrate

Supplier: Thermo Scientific

Description: Ethyl-2-hydroxyisobutyrate ≥98%

MSDS

Supplier: Apollo Scientific

Description: Ethyl-2-hydroxyisobutyrate 98%

Catalog Number: (ACRO436180050)

Supplier: Thermo Scientific

Description: Methyl (R)-(-)-3-hydroxyisobutyrate 98%

UOM: 1 * 5 g

MSDS Sale

Supplier: Apollo Scientific

Description: Methyl-2-hydroxyisobutyrate 95%

Supplier: Apollo Scientific

Description: Methyl (R)-(-)-3-hydroxyisobutyrate 97%

Supplier: Thermo Scientific

Description: 2-Hydroxyisobutyric acid 98%

MSDS

Catalog Number: (BOSSBS-15483R-HRP)

Supplier: Bioss

Description: HIBADH is a 336 amino acid mitochondrial enzyme that catalyses the NAD+-dependent, reversible oxidisation of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7,0 and 10,0, with optimal activity between 8,8 and 9,0. It was previously hypothesised that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterised by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.

UOM: 1 * 100 µl

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Supplier: Apollo Scientific

Description: 2-Hydroxyisobutyric acid

Supplier: Thermo Scientific

Description: 2-Hydroxyisobutyric acid, (max. 2% H₂O) 99% (dry weight)

MSDS Certificates

Supplier: Thermo Scientific

Description: Appearance: Clear colorless Liquid

MSDS

Supplier: Apollo Scientific

Description: (R)-3,3,3-Trifluoro-2-hydroxy-2-methylpropionic acid 97%

Catalog Number: (BOSSBS-15483R)

Supplier: Bioss

Description: HIBADH is a 336 amino acid mitochondrial enzyme that catalyzes the NAD+-dependent, reversible oxidization of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7.0 and 10.0, with optimal activity between 8.8 and 9.0. It was previously hypothesized that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterized by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.

UOM: 1 * 100 µl

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Catalog Number: (BOSSBS-15483R-CY7)

Supplier: Bioss

Description: HIBADH is a 336 amino acid mitochondrial enzyme that catalyses the NAD+-dependent, reversible oxidisation of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7,0 and 10,0, with optimal activity between 8,8 and 9,0. It was previously hypothesised that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterised by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.

UOM: 1 * 100 µl

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Catalog Number: (BOSSBS-15483R-A647)

Supplier: Bioss

Description: HIBADH is a 336 amino acid mitochondrial enzyme that catalyses the NAD+-dependent, reversible oxidisation of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7,0 and 10,0, with optimal activity between 8,8 and 9,0. It was previously hypothesised that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterised by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.

UOM: 1 * 100 µl

Sale

Catalog Number: (BOSSBS-15483R-A488)

Supplier: Bioss

Description: HIBADH is a 336 amino acid mitochondrial enzyme that catalyses the NAD+-dependent, reversible oxidisation of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7,0 and 10,0, with optimal activity between 8,8 and 9,0. It was previously hypothesised that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterised by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.

UOM: 1 * 100 µl

Sale

Catalog Number: (BOSSBS-15483R-A750)

Supplier: Bioss

Description: HIBADH is a 336 amino acid mitochondrial enzyme that catalyses the NAD+-dependent, reversible oxidisation of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7,0 and 10,0, with optimal activity between 8,8 and 9,0. It was previously hypothesised that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterised by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.

UOM: 1 * 100 µl

Sale